Congenital coronary arterial fistula

**Definition:** A congenital cardiovascular malformation in which a coronary artery communicates, through an anomalous channel, with a cardiac chamber or with any segment of the systemic or pulmonary circulation.

Additional information: this communication may be simple and direct or may be tortuous and dilated. In order of frequency the involved coronary artery is the right, the left and, rarely, both coronary arteries. Occasionally multiple fistulas are present.

**Inclusions:** - congenital coronary fistula to pulmonary artery

**Exclusions:** - anomalous origin of coronary artery from pulmonary arterial tree