I270Level 3
Primary pulmonary hypertension
**Inclusion terms:** - Heritable pulmonary arterial hypertension - Idiopathic pulmonary arterial hypertension - Primary group 1 pulmonary hypertension - Primary pulmonary arterial hypertension
**Excludes1:** - persistent pulmonary hypertension of newborn (P29.30) - pulmonary hypertension NOS (I27.20) - secondary pulmonary arterial hypertension (I27.21) - secondary pulmonary hypertension (I27.29)
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