4A00.1Level 4

Defects in the complement system

**Exclusions:** - Atypical haemolytic uraemic syndrome - Paroxysmal nocturnal haemoglobinuria

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4A00.10Immunodeficiency with an early component of complement deficiency

4A00.11Immunodeficiency with a late component of complement deficiency

4A00.12Immunodeficiency with factor B deficiency

4A00.13Immunodeficiency with factor D anomaly

4A00.14Hereditary angioedema

4A00.15Acquired angioedema

4A00.1YOther specified defects in the complement system

4A00.1ZDefects in the complement system, unspecified

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