4A41.21LeafLevel 5
Noninflammatory inclusion body myopathy
**Definition:** Noninflammatory inclusion body myopathy (IBM) is an idiopathic muscle disorder without inflammatory exudates and expression of class I major histocompatibility complex. Rimmed vacuoles and “IBM-like” filaments without inflammatory cells are described in muscle biopsy.
**Exclusions:** - Myasthenia gravis or certain specified neuromuscular junction disorders
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/api/v1/systems/icd_11/nodes/4A41.21Cross-system equivalences0
No cross-system equivalences mapped for this node.