Mitochondrial Processing Peptidase

**Definition:** A hetero-dimeric protein consisting of two subunits, alpha and beta, which are referred to as PMPCA and PMPCB in humans. It plays an essential role in removing the N-terminal targeting peptidase from precursor proteins imported into the mitochondria.

**Tree numbers:** - D08.811.277.656.300.480.563 - D08.811.277.656.675.374.563 - D12.776.575.758

**Synonyms:** - Matrix Processing Peptidase - Mitochondrial Processing Protease