Blastic Plasmacytoid Dendritic Cell Neoplasm

**Definition:** A rare and aggressive hematologic malignancy derived from the precursors of PLASMACYTOID DENDRITIC CELLS. Blastic plasmacytoid dendritic cell neoplasms affect bone marrow and blood in addition to the lymph nodes, spleen, central nervous system, and skin.

**Tree numbers:** - C04.557.227.001 - C04.557.337.001 - C04.557.386.001 - C04.588.448.001 - C04.588.805.175 - C15.378.400.001 - C17.800.882.001

**Synonyms:** - Agranular CD4+ CD56+ Hematodermic Neoplasm-Tumor - Agranular CD4+ Natural Killer Cell Leukemia - Blastic Natural Killer Leukemia - Blastic Natural Killer Lymphoma - Blastic NK Cell Lymphoma - Blastic NK-Cell Lymphoma - CD4+-CD56+ Hematodermic Neoplasm - BPDCN - Monomorphic NK-Cell Lymphoma