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D000099105Level 5

Autoimmune Inner Ear Disease

**Definition:** Inner ear diseases caused by autoimmune reaction, characterized by audiovestibular dysfunction including TINNITUS; VERTIGO and progressive SENSORINEURAL HEARING LOSS. Autoimmune inner ear disease may coexist with other systemic autoimmune diseases (e.g., COGAN SYNDROME).

**Tree numbers:** - C09.218.568.001 - C20.111.281

**Synonyms:** - Autoimmune Inner Ear Disorders - Autoinflammatory Inner Ear Disorders - Immune-Mediated Inner Ear Disease - Immune-Mediated Inner Ear Disorders

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