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D000746Level 7

Anemia, Hemolytic, Congenital Nonspherocytic

**Definition:** Any one of a group of congenital hemolytic anemias in which there is no abnormal hemoglobin or spherocytosis and in which there is a defect of glycolysis in the erythrocyte. Common causes include deficiencies in GLUCOSE-6-PHOSPHATE ISOMERASE; PYRUVATE KINASE; and GLUCOSE-6-PHOSPHATE DEHYDROGENASE.

**Tree numbers:** - C15.378.050.141.150.100 - C16.320.070.100

**Synonyms:** - Anemia, Congenital Nonspherocytic Hemolytic - Anemia, Hemolytic Congenital, Nonspherocytic - Congenital Nonspherocytic Hemolytic Anemia - Hemolytic Anemia, Congenital Nonspherocytic

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