D001123Level 7
Argininosuccinate Lyase
**Definition:** An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.
**Tree numbers:** - D08.811.520.232.300.400
**Synonyms:** - Argininosuccinase
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