D001506Level 5
Beckwith-Wiedemann Syndrome
**Definition:** A syndrome of multiple defects characterized primarily by umbilical hernia (HERNIA, UMBILICAL); MACROGLOSSIA; and GIGANTISM; and secondarily by visceromegaly; HYPOGLYCEMIA; and ear abnormalities.
**Tree numbers:** - C16.131.077.133 - C16.131.260.080 - C16.320.180.080 - C16.320.447.375
**Synonyms:** - EMG Syndrome - Exomphalos-Macroglossia-Gigantism Syndrome - Wiedemann-Beckwith Syndrome - Wiedemann-Beckwith Syndrome (WBS) - Wiedemann Syndrome
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