D001606Level 6
Bernard-Soulier Syndrome
**Definition:** A familial coagulation disorder characterized by a prolonged bleeding time, unusually large platelets, and impaired prothrombin consumption.
**Tree numbers:** - C15.378.100.100.080 - C15.378.140.120 - C15.378.463.080 - C16.320.099.080
**Synonyms:** - Giant Platelet Syndrome
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