D005164Level 4
Factor IX
**Definition:** Storage-stable blood coagulation factor acting in the intrinsic pathway of blood coagulation. Its activated form, IXa, forms a complex with factor VIII and calcium on platelet factor 3 to activate factor X to Xa. Deficiency of factor IX results in HEMOPHILIA B (Christmas Disease).
**Tree numbers:** - D08.622.355 - D12.776.124.125.375 - D12.776.811.243.355 - D23.119.375
**Synonyms:** - Factor Nine - Autoprothrombin II - Christmas Factor - Coagulation Factor IX - Plasma Thromboplastin Component - Blood Coagulation Factor IX - Factor IX Complex - Factor 9 - Factor IX Fraction
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