D005677Level 8
G(M1) Ganglioside
**Definition:** A specific monosialoganglioside that accumulates abnormally within the nervous system due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis.
**Tree numbers:** - D09.400.410.420.025.475.390 - D10.390.470.025.475.390 - D10.570.877.360.025.475.390
**Synonyms:** - GM1 Ganglioside - Monosialosyl Tetraglycosyl Ceramide
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