G(M3) Ganglioside

**Definition:** A ganglioside present in abnormally large amounts in the brain and liver due to a deficient biosynthetic enzyme, G(M3):UDP-N-acetylgalactosaminyltransferase. Deficiency of this enzyme prevents the formation of G(M2) ganglioside from G(M3) ganglioside and is the cause of an anabolic sphingolipidosis.

**Tree numbers:** - D09.400.410.420.025.475.510 - D10.390.470.025.475.510 - D10.570.877.360.025.475.510

**Synonyms:** - II3NeuAcLacCer - Sialyl Lactosylceramide - Hematoside - Sialyllactosylceramide - Ganglioside GM3