D005698Level 7
Galactosylceramidase
**Definition:** An enzyme that hydrolyzes galactose from ceramide monohexosides. Deficiency of this enzyme may cause globoid cell leukodystrophy (LEUKODYSTROPHY, GLOBOID CELL). EC 3.2.1.46.
**Tree numbers:** - D08.811.277.450.410.120
**Synonyms:** - Galactocerebrosidase - Galactosylceramide beta-Galactosidase - Galactosylceramide Galactosidase - Galactosylcerebroside beta-Galactosidase
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