Granuloma, Lethal Midline

**Definition:** A condition that is characterized by inflammation, ulceration, and perforation of the nose and the PALATE with progressive destruction of midline facial structures. This syndrome can be manifested in several diseases including the nasal type of EXTRANODAL NK-T-CELL LYMPHOMA and GRANULOMATOSIS WITH POLYANGIITIS.

**Tree numbers:** - C08.460.393 - C09.603.393

**Synonyms:** - Lethal Midline Granuloma