UDPglucose-Hexose-1-Phosphate Uridylyltransferase

**Definition:** An enzyme that catalyzes the transfer of UMP from UDPglucose to galactose 1-phosphate, forming UDPgalactose and glucose 1-phosphate. Deficiency in this enzyme is the major cause of GALACTOSEMIA. EC 2.7.7.12.

**Tree numbers:** - D08.811.913.696.445.850

**Synonyms:** - Galactose-1-P-Uridyltransferase - Hexosephosphate Uridylyltransferase - Uridyl Transferase - Phosphogalactose Uridyl Transferase