World Of Taxonomy
D007790Level 5

Lactosylceramides

**Definition:** Glycosphingolipids which contain as their polar head group a lactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in lactosylceramide beta-galactosidase, is the cause of lactosylceramidosis.

**Tree numbers:** - D02.065.313.612 - D09.400.410.420.525.200.612 - D10.390.470.675.200.612 - D10.570.877.360.612.200.612

**Synonyms:** - Lactosyl Ceramides

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