D008203Level 5
Lymphangiomyoma
**Definition:** A tumorlike condition characterized by SMOOTH MUSCLE and ENDOTHELIUM proliferation of LYMPHATIC VESSELS and LYMPH NODES in the MEDIASTINUM and retroperitoneum, also in the lung. It may be manifested by chylous PLEURAL EFFUSION and ASCITES.
**Tree numbers:** - C04.557.375.460 - C15.604.515.562 - C20.683.515.710
**Synonyms:** - Lymphangioleiomyoma
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