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D008556Level 5

Melkersson-Rosenthal Syndrome

**Definition:** An idiopathic syndrome characterized by one or more of the following; recurrent orofacial swelling, relapsing facial paralysis, and fissured tongue (lingua plicata). The onset is usually in childhood and relapses are common. Cheilitis granulomatosa is a monosymptomatic variant of this condition. (Dermatol Clin 1996 Apr;14(2):371-9; Magalini & Magalini, Dictionary of Medical Syndromes, 4th ed, p531)

**Tree numbers:** - C07.465.299.800 - C07.465.466 - C10.292.319.800

**Synonyms:** - Melkerson-Rosenthal Syndrome - Rosenthal-Melkerson Syndrome - Syndrome, Melkerson Rosenthal - Cheilitis Granulomatosa, Facial Neuropathy, Orofacial Edema - Cheilitis Granulomatosa, Orofacial Edema, Facial Neuropathy - Facial Neuropathy, Cheilitis Granulomatosa, Orofacial Edema - Facial Neuropathy, Orofacial Edema, Cheilitis Granulomatosa - Macrocheilia, Facial Palsy, Edema - Miescher-Melkersson-Rosenthal Granulomatous Cheilitis - Orofacial Edema, Cheilitis Granulomatosa, Facial Neuropathy - Orofacial Edema, Facial Neuropathy, Cheilitis Granulomatosa - Melkersson Syndrome - Rosenthal-Melkersson Syndrome - Melkersson-Rosenthal-Miescher Syndrome

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