Ornithine Carbamoyltransferase

**Definition:** A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3.

**Tree numbers:** - D08.811.913.555.275.600

**Synonyms:** - Ornithine Carbamylphosphate Transferase - Ornithine Transcarbamylase