Phenylalanine Hydroxylase

**Definition:** An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.

**Tree numbers:** - D08.811.682.690.708.601

**Synonyms:** - Phenylalanine 4-Monooxygenase - Phenylalanine 4-Hydroxylase