D011553Level 8
Pseudomyxoma Peritonei
**Definition:** A peritoneal adenocarcinoma characterized by build-up of MUCUS in the PERITONEAL CAVITY. Mucus secreting cells may attach to the peritoneal lining and continue to secrete mucus. The majority of cases represent tumor spread from a primary low-grade mucinous neoplasm of the APPENDIX (NCI Thesaurus).
**Tree numbers:** - C04.557.470.200.025.075.500 - C04.557.470.590.075.500
**Synonyms:** - Ascites, Gelatinous - Gelatinous Ascites - Syndrome of Pseudomyxoma Peritonei
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