Trihexosylceramides

**Definition:** Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in ceramide trihexosidase, is the cause of angiokeratoma corporis diffusum (FABRY DISEASE).

**Tree numbers:** - D02.065.313.906 - D09.400.410.420.525.200.906 - D10.390.470.675.200.906 - D10.570.877.360.612.200.906

**Synonyms:** - Ceramide Trihexosides - Trihexosyl Ceramides