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D014607Level 4

Uveomeningoencephalitic Syndrome

**Definition:** A syndrome characterized by bilateral granulomatous UVEITIS with IRITIS and secondary GLAUCOMA, premature ALOPECIA, symmetrical VITILIGO, poliosis circumscripta (a strand of depigmented hair), HEARING DISORDERS, and meningeal signs (neck stiffness and headache). Examination of the cerebrospinal fluid reveals a pattern consistent with MENINGITIS, ASEPTIC. (Adams et al., Principles of Neurology, 6th ed, p748; Surv Ophthalmol 1995 Jan;39(4):265-292)

**Tree numbers:** - C10.114.843 - C11.941.879.980 - C20.111.258.925

**Synonyms:** - Vogt-Koyanagi-Harada Syndrome - Uveomeningoencephalitis - Syndrome, Vogt Koyanagi Harada - Syndrome, VKH (Vogt Koyanagi Harada) - Vogt-Koyanagi-Harada Disease - VKH (Vogt Koyanagi Harada) Syndrome - VKH Syndrome

GET/api/v1/systems/mesh/nodes/D014607
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