Xanthogranuloma, Juvenile

**Definition:** Benign disorder of infants and children caused by proliferation of HISTIOCYTES, macrophages found in tissues. These histiocytes, usually lipid-laden non-Langerhans cells, form multiple yellow-red nodules most often in the skin, the eye, and sometimes in the viscera. Patients appear to have normal lipid metabolism and are classified as a normolipemic non-Langerhans cell histiocytosis.

**Tree numbers:** - C15.604.250.410.900 - C17.800.973

**Synonyms:** - Nevoxanthoendothelioma - Xanthoma, Juvenile