Ichthyosis, X-Linked

**Definition:** Chronic form of ichthyosis that is inherited as a sex-linked recessive trait carried on the X-chromosome and transmitted to the male offspring. It is characterized by severe scaling, especially on the extremities, and is associated with steroid sulfatase deficiency.

**Tree numbers:** - C16.131.831.512.420 - C16.320.322.241 - C16.320.565.925.400 - C16.320.850.408 - C16.614.492.420 - C17.800.428.333.420 - C17.800.804.512.420 - C17.800.827.408 - C18.452.648.925.400

**Synonyms:** - Ichthyosis, Sex-Linked