Porphyria Cutanea Tarda

**Definition:** An autosomal dominant or acquired porphyria due to a deficiency of UROPORPHYRINOGEN DECARBOXYLASE in the LIVER. It is characterized by photosensitivity and cutaneous lesions with little or no neurologic symptoms. Type I is the acquired form and is strongly associated with liver diseases and hepatic toxicities caused by alcohol or estrogenic steroids. Type II is the familial form.

**Tree numbers:** - C06.552.830.100 - C16.320.850.742.250 - C17.800.827.742.250 - C18.452.811.400.250