Neuroectodermal Tumors, Primitive, Peripheral

**Definition:** A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with EWING SARCOMA.

**Tree numbers:** - C04.557.465.625.600.590.650 - C04.557.470.670.590.650 - C04.557.580.625.600.590.650

**Synonyms:** - Peripheral Primitive Neuroectodermal Neoplasm - Primitive Neuroectodermal Tumor, Extracranial - Neuroepithelioma, Peripheral - Peripheral Primitive Neuroectodermal Tumor - Neuroectodermal Tumor, Peripheral - Peripheral Primitive Neuroectodermal Tumors - (pPNET) Peripheral Primitive Neuroectodermal Tumors - Extracranial Primitive Neuroectodermal Tumor - Neuroectodermal Tumor, Peripheral Primitive - Neuroectodermal Neoplasm, Peripheral Primitive