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D018549Level 8

Cryptogenic Organizing Pneumonia

**Definition:** An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a pneumonia-like illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.

**Tree numbers:** - C08.127.446.135.140.600.750 - C08.381.483.652.500.750.249 - C08.381.495.146.135.140.600.750

**Synonyms:** - Primary Organizing Pneumonia - BOOP Bronchiolitis Obliterans Organizing Pneumonia - Bronchiolitis Obliterans Organizing Pneumonia

GET/api/v1/systems/mesh/nodes/D018549
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