Unverricht-Lundborg Syndrome

**Definition:** An autosomal recessive condition characterized by recurrent myoclonic and generalized seizures, ATAXIA, slowly progressive intellectual deterioration, DYSARTHRIA, and intention tremor. Myoclonic seizures are severe and continuous, and tend to be triggered by movement, stress, and sensory stimuli. The age of onset is between 8 and 13 years, and the condition is relatively frequent in the Baltic region, especially Finland. (From Menkes, Textbook of Child Neurology, 5th ed, pp109-110)

**Tree numbers:** - C10.228.140.490.375.130.650.900 - C10.228.140.490.493.063.650.900 - C10.574.500.875 - C16.320.400.940

**Synonyms:** - Baltic Myoclonus - Mediterranean Myoclonic Epilepsy - Baltic Myoclonus Epilepsy - Unverricht Disease - Myoclonus Progressive Epilepsy of Unverricht and Lundborg - Epilepsy, Progressive Myoclonic Type 1 - Epilepsy, Progressive Myoclonus 1 - Myoclonic Epilepsy of Unverricht and Lundborg - Progressive Myoclonus Epilepsybaltic Myoclonic Epilepsy - Epilepsy, Progressive Myoclonic 1 - Epilepsy, Progressive Myoclonic 1a - Baltic Myoclonic Epilepsy - Unverricht-Lundborg Disease - Lundborg-Unverricht Syndrome - Progressive Myoclonus Epilepsy 1