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D020331Level 5

Mobius Syndrome

**Definition:** A syndrome of congenital facial paralysis, frequently associated with abducens palsy and other congenital abnormalities including lingual palsy, clubfeet, brachial disorders, cognitive deficits, and pectoral muscle defects. Pathologic findings are variable and include brain stem nuclear aplasia, facial nerve aplasia, and facial muscle aplasia, consistent with a multifactorial etiology. (Adams et al., Principles of Neurology, 6th ed, p1020)

**Tree numbers:** - C07.465.299.825 - C10.292.319.825 - C10.292.562.700.375.750 - C11.590.436.400.750 - C16.131.077.578 - C16.614.595

**Synonyms:** - Moebius Spectrum - Möbius Sequence - Moebius Syndrome - Congenital Oculofacial Paralysis, Moebius - Moebius Congenital Oculofacial Paralysis - Moebius Sequence - Congenital Ophthalmoplegia and Facial Paresis

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