D034062Level 5
Insomnia, Fatal Familial
**Definition:** An autosomal dominant disorder characterized by degeneration of the THALAMUS and progressive insomnia. It is caused by a mutation in the prion protein (PRIONS).
**Tree numbers:** - C01.207.800.392 - C10.228.228.800.392 - C10.574.843.512 - C10.886.425.800.800.400
**Synonyms:** - Fatal Familial Insomnia - Insomnia Familial Fatal - Familial Fatal Insomnia
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