gamma-Butyrobetaine Dioxygenase

**Definition:** An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.

**Tree numbers:** - D08.811.682.690.708.401

**Synonyms:** - gamma-Butyrobetaine,2-Oxoglutarate Dioxygenase - Trimethylaminobutyrate Hydroxylase - gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase - 4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating) - Butyrobetaine Hydroxylase - gamma-Butyrobetaine Hydroxylase