D050645Level 7
2-Oxoisovalerate Dehydrogenase (Acylating)
**Definition:** An NAD+ dependent enzyme that catalyzes the oxidation 3-methyl-2-oxobutanoate to 2-methylpropanoyl-CoA. It plays a role in the degradation of VALINE; LEUCINE; and ISOLEUCINE.
**Tree numbers:** - D08.811.682.657.350.825
**Synonyms:** - 2-Oxoisovalerate Dehydrogenase - alpha-Ketoisovalerate Dehydrogenase
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