Glutaryl-CoA Dehydrogenase

**Definition:** A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.

**Tree numbers:** - D08.811.682.660.425

**Synonyms:** - Glutaryl CoA Dehydrogenase - Glutaryl-Coenzyme A Dehydrogenase