Lipodystrophy, Congenital Generalized

**Definition:** Congenital disorders, usually autosomal recessive, characterized by severe generalized lack of ADIPOSE TISSUE, extreme INSULIN RESISTANCE, and HYPERTRIGLYCERIDEMIA.

**Tree numbers:** - C16.320.565.398.745 - C17.800.849.391.550 - C18.452.584.563.745 - C18.452.584.625.550 - C18.452.648.398.745 - C18.452.880.391.550

**Synonyms:** - Congenital Generalized Lipodystrophy - Berardinelli-Seip Congenital Lipodystrophy - Brunzell Syndrome (with Bone Cysts) - Generalized Lipodystrophy - Total Lipodystrophy - Berardinelli-Seip Syndrome