Persistent Hyperplastic Primary Vitreous

**Definition:** A developmental ocular anomaly in which the primary VITREOUS BODY and its surrounding hyaloid vasculature failed to regress. It is usually unilateral and characterized by CATARACT; MICROPHTHALMOS (small eyeballs), and retrolenticular fibrovascular tissue. (from Yanoff: Ophthalmology, 2nd ed.)

**Tree numbers:** - C11.250.616 - C16.131.384.725

**Synonyms:** - Persistent Fetal Vasculature Syndrome - Persistent Hyaloid Artery - Persistent Hyaloid Vasculature