Hexosaminidase B

**Definition:** A mammalian beta-hexosaminidase isoform that is comprized of hexosaminidase beta subunits. Deficiency of hexosaminidase B due to mutations in the gene encoding the hexosaminidase beta subunit is a case of SANDHOFF DISEASE.

**Tree numbers:** - D08.811.277.450.483.180.875

**Synonyms:** - Hex B