Perivascular Epithelioid Cell Neoplasms

**Definition:** A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. These cells do not have a normal anatomic homolog. (From Fletcher CDM, et. al., World Health Organization Classification of Tumors: Pathology and Genetics of Tumors of Soft Tissue and Bone, 2002).

**Tree numbers:** - C04.557.450.692

**Synonyms:** - Neoplasms, Perivascular Epithelioid Cell - PEComa - Perivascular Epithelioid Cell Tumors - Perivascular Epithelioid Cell Neoplasm - Perivascular Epithelioid Cell Tumor - PEComas