Hereditary Angioedema Type III

**Definition:** A form of hereditary angioedema that occurs in women and is precipitated or worsened by high ESTROGEN levels. It is associated with mutations in the gene for FACTOR XII that result in its increased activity.

**Tree numbers:** - C14.907.079.500.500 - C17.800.862.945.066.500.500 - C20.543.480.904.066.500.500

**Synonyms:** - Estrogen-Sensitive Hereditary Angioedema - Estrogen-Related HAE - Estrogen-Sensitive HAE - Angioedema, Hereditary, Type III - HAE with Normal C1 Inhibitor Concentration and Function - Angioneurotic Edema, Hereditary, with Normal C1 Inhibitor Concentration and Function - Hereditary Angioedema with Normal C1 Inhibitor Activity