Kasabach-Merritt Syndrome

**Definition:** Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

**Tree numbers:** - C04.557.645.375.617 - C15.378.140.855.645 - C15.378.243.937.645

**Synonyms:** - Kasabach-Merritt Phenomenon - Hemangioma Thrombocytopenia Syndrome - Thrombocytopenia-Hemangioma Syndrome - Hemangioma-Thrombocytopenia Syndrome