Steatocystoma Multiplex

**Definition:** A disorder characterized by multiple, wide spread cutaneous cysts that often become inflamed and rupture. It is caused by the same mutations in the gene coding for KRT-17 that are causative mutations for Pachyonychia congenita, Type 2. Natal teeth involvement is sometimes associated with steatocystoma multiplex.

**Tree numbers:** - C16.131.831.350.856.500 - C16.320.850.250.856.500 - C17.800.529.594.500 - C17.800.804.350.856.500 - C17.800.827.250.856.500

**Synonyms:** - Sebaceous Cysts, Multiple - Multiple Sebaceous Cysts - Multiplex Steatocystoma