Mitochondrial Trifunctional Protein

**Definition:** A mitochondrial protein consisting of four alpha-subunits and four beta-subunits. It contains enoyl-CoA hydratase, long-chain-3-hydroxyacyl-CoA dehydrogenase, and acetyl-CoA C-acyltransferase activities and plays an important role in the metabolism of long chain FATTY ACIDS.

**Tree numbers:** - D08.811.520.241.300.250.249 - D08.811.641.765 - D08.811.682.047.820.150.707.249 - D08.811.913.050.080.249 - D12.776.543.602 - D12.776.575.765

**Synonyms:** - Mitochondrial Long Chain Enoyl CoA Hydratase 3 Hydroxyacyl CoA Dehydrogenase 3 Ketoacyl CoA Thiolase Trifunctional Protein - FA beta-OMC - Mitochondrial Fatty Acid beta-Oxidation Trifunctional Protein