Maturity-Onset Diabetes of the Young

**Semantic type:** Disease or Syndrome

**Definition:** A rare autosomal dominant form of diabetes mellitus affecting young people with a positive family history. MODY is a form of monogenic diabetes, resulting from mutations in a single gene. The most common forms are HNF1alpha-MODY (MODY3) and GCK-MODY (MODY2), due to mutations in the HNF1A and GCK genes, respectively.

**Synonyms:** - MODY - Maturity Onset Diabetes of the Young