C116380Level 4
Chronic Infantile Neurological Cutaneous and Articular Syndrome
**Semantic type:** Disease or Syndrome
**Definition:** A congenital autoinflammatory disorder that presents within a few days of birth and is characterized by a clinical triad of skin rash, chronic meningitis, and joint pain with recurrent fever and inflammation.
**Synonyms:** - CINCA - CINCA Syndrome - CINCA/NOMID - NOMID - Neonatal-Onset Multisystem Inflammatory Disease - Neonatal-Onset Multisystem Inflammatory Disease
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