Benign Notochordal Cell Tumor

**Semantic type:** Neoplastic Process

**Definition:** An intraosseous benign tumor of notochord origin that arises in the bones of the base of the skull, vertebral bodies, sacrum or coccyx. It contains vacuolated tumor cells without atypia, but lacks myxoid matrix, necrosis, and lobular architecture, which are features that characterize its malignant counterpart, chordoma. Most lesions are incidental findings.

**Synonyms:** - BNCT - Intraosseous Benign Notochordal Cell Tumor