Pauci-Immune Glomerulonephritis associated with Granulomatosis with Polyangiitis

**Semantic type:** Disease or Syndrome

**Definition:** Glomerulonephritis in the context of granulomatosis with polyangiitis in which anti-neutrophil cytoplasm antibody (ANCA) is almost always present.

**Synonyms:** - Pauci-immune Glomerulonephritis associated with Granulomatosis with Polyangiitis