Pseudohypoaldosteronism Type 1

**Semantic type:** Disease or Syndrome

**Definition:** A hereditary, heterogeneous disorder of electrolyte metabolism that is characterized by renal resistance to aldosterone action, resulting in salt wasting, hypotension, hyperkalemia, and metabolic acidosis.

**Synonyms:** - PHA1B - Pseudohypoaldosteronism Type I Autosomal Recessive