C123906Level 8
Childhood Gastrointestinal Stromal Tumor
**Semantic type:** Neoplastic Process
**Definition:** A gastrointestinal stromal tumor (GIST) occurring in childhood. Pediatric GISTs differ biologically from adult GISTs in that only 11% of pediatric GISTs have activating mutations of KIT and PDGFRA.
**Synonyms:** - Childhood GIST - Childhood GIST - Gastrointestinal Stromal Tumor (GIST)
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